CDH - Congenital Dislocation of the Hip: Mamoun Kremli, Professor/Consultant Pediatric Orthopedics
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Presentation Transcript
CDHCongenital Dislocation of the Hip Mamoun Kremli Professor / Consultant Pediatric Orthopedics College of Medicine & King Khalid University Hospital
CDH • The most common disorder affecting the hip in children • Spectrum of diseases/abnormalities of the hip with different etiologies, pathologies, and natural histories affecting the proximal femur and acetabulum • Initial pathology is congenital, progresses if untreated. • Does not always result in dislocation.
CDHDefinition • A progressive deformation of previously normally formed structures during the embryonic period NOT A malformation arising during the period of organogenesis
CDHNomenclature • CDH Congenital Dislocation of the Hip • DDH Developmental Dysplasia of the Hip • CDH Congenital Dysplasia of the Hip • CHD Congenital Heart Disease !
CDH Spectrum • Teratologic Hip : Fixed dislocation Occurrs prenatally Often with other anomalies • Dislocated Hip : Completely out May or may not be reducible • Subluxated Hip : Only partially in • Unstable Hip : Femoral head can be dislocated • Acetabular Dysplasia : Shallow Acetabulu Head Subluxated or in place
CDHIncidence • Hip Instability at Birth : 0.5 – 1 % of infants • Classic CDH : 0.1 % of infants • Mild Dysplasia : Substantial Contributing to adult Osteoarthritis Up to 50 % of Hip Arthritis in Ladies Have underlying hip dysplasia
CDHEtiology Multi-factorial
CDHEtiology Physiologic Factors Ligament Laxity : Hormonal : ( Estrogen, Relaxin) Females Familial hyper laxity : mild - moderate - Ehler Danlos ADD Picture of knee hyperextension
CDHEtiology Genetic Factors • Gender :Female Most studies: Females > 4-6 X than males • Twin studies: Monozygotic 38 % Dizygotic 3 % (similar to siblings)
CDHEtiology Family Incidence and Genetic Counselling
CDHEtiology Mechanical Factors Prenatal : - Breech position - Oligohydramnious - Primigravida - Cong. Knee recurvatum/dislocation - Metatarsus adductus - Torticollis Postnatal : - Swaddling / Strapping – Knees extended
CDHEtiologyMechanical Factors • Breech Presentation : Normally 2 –4 % CDH 16 % The Breech positionIn Utero Extended knees and flexed hips
CDHEtiologyEnvironmental & Mechanical Factors • Swaddling / strapping ( Mihad ): Knees extended & Hips adducted • Proven experimentally • Proven statistically • American Indians. • Eskimos, and • Saudi Arabia • Mechanics • Hip adduction and extension
CDHPatients At Risk • Positive Family History : increases risk 10X • A baby girl : increases risk 4-6 times • Breech Presentation : increases risk 5-10 X • Torticollis : CDH in 10-20 % cases • Foot Deformities : ( calcaneovalgus & metatarsus adductus) signs of intrauterine crowding • Knee Deformities : ( hyperextension & dislocation ) associated with Teratologic type
CDH Risk FactorsWhen Risk Factors Are Present • The infant should be examined repeatedly • The hip should be imaged ( by U/S or X-ray )
CDHNeonatal Examination The infant should be quiet and comfortable
CDHNeonatal Examination LOOK : • External rotation attitude • Lateralized contour • Wide perineum • ( in bilateral )
CDHNeonatal Examination LOOK : • Asymmetric thigh folds anterior posterior
CDHClinical Examination • Look : Shortening ( not in neonates ) -in supine - Galeazzy sign
CDHNeonatal Examination FEEL : • Empty groin • Weak Femoral pulse
CDHNeonatal Examination MOVE : • Hip instability in early infancy • Limited hip abduction in flexion - later (careful in bilateral) if <600 on both sides: request imaging
Cerebral palsyClinical AssessmentHip Flexion Deformity SPECIAL : • Loss of fixed flexion deformity of hips ( early infancy ) • Normally FFD newborn 28o at 6 weeks 19o at 6 months 7o Thomas Test FFD Normal No FFD ?CDH
CDHNeonatal ExaminationOrtolani Feel a Clunk Not hear a click !
CDHNeonatal ExaminationOrtolani / Barlow clunk Ortolani Barlow
CDHNeonatal ExaminationOrtolani / Barlow Ortolani Barlow
CDHNeonatal ExaminationHamstring Stretch Sign • Flex hip and knee 900 each. • Keep hip flexed and gradually extend the knee • Normally a resistance is felt towards the end of knee extension (caused by the hamstrings which are pulled from both ends) • In cases of CDH, no resistance is felt (when the hip is dislocated, the origin of the hamstrings are not pulled by hip flexion)
CDHClinical Examination • Neonate (up to 2-3 months) : - Instability/ Ortolani-Barlow - Thomas test • Infant ( > 2-3 months) : - Limited abduction - Shortening ( Galeazzi ) - Hamstring stretch sign • Toddler : - Limited abduction - Shortening ( Galeazzi ) - Hamstring stretch sign • Walking : - Trendelenburgh - Hamstring stretch sign
CDHClinical ExaminationThe Walking Child • Trendelenburgh: unilateral / bilateral (waddling)
CDHScreening Program • Clinical screening proven to be effective • Performed by Trained personnel • Must be DYNAMIC with periodic examination till walking • Adjunctive use of U/S controversial
CDHUltrasound Screening • Incidence of hip instability declines rapidly to 50 % within the first week of neonatal life • Better to delay U/S screening
CDHUltrasound Screening • Early U/S screening not recommended • Delayed U/S screening : -Older than 6 weeks -Those at risk only - by History Clinical exam
CDHUltrasound Referral • If hip normal : no need • If hip clearly unstable : no need • If suspicious : U/S appropriate • If at risk factors : U/S appropriate
CDHUltrasound • Too sensitive detects a lot of hip anomalies most of which would develop normally • Operator dependant Static Vs Dynamic
CDHRadiography • Early infancy : not reliable • By 2-3 months of age : reliable AP view - neutral position - draw reference lines - acetabular index - in early infancy < 30o : normal 30o – 40o : questionable > 40o : abnormal Von Rosen view : 45o abduction
CDHRadiography in out out in Von Rosen view
CDHRadiography 39o 27o
CDHRadiography out in
CDHTreatmentAims • Obtain and Maintain concentric reduction • In an Atruamatic fashion • Without disrupting the blood supply
CDHTreatment • Method depends onAge • The earlier started, the easier the treatment • The earlier started, the better the results • Should be detected EARLY
CDHTreatment • Birth to 6 months : Pavlik harness or hip spica cast • 6 months – 12 months : closed reduction UGA and hip spica casts • 12 months – 18 months : possible closed / possible open reduction • Above 18 months : open reduction and ? Acetabuloplasty • Above 2 years : open reduction,acetabulplasty, and femoral osteotomy • Above 8 years : open reduction,acetabulplasty cutting three bones, and femoral osteotomy
CDHTreatmentHip instability in the neonatal period Most resolve spontaneously • Observation • Pavlik harness • Double /triple diapers ??