1. For Excretion Urea HMDB00294 UREA CYCLE AND METABOLISM OF AMINO ACIDS – ARGININOSUCCINIC ACIDURIA In Homo sapiens Alanine Aspartate Metabolism Accumulation Citrate Cycle Argininosuccinic acid HMDB00052 Pyrimidine metabolism L-Asparticacid HMDB00191 argininosuccinate synthetase 1 P00966 argininosuccinate lyase P04424 Fumaric acid HMDB00134 Nitrogen metabolism Arginine Metabolism Citrulline HMDB00904 D-Arg & D-Orn Metabolism N-Acetylornithine HMDB03357 L-Arginine HMDB00517 Carbamoylphosphate HMDB01096 Ammonia HMDB00051 carbamoyl-phosphate synthetase 1, mitochondrial P31327 aminoacylase 1 Q03154 arginine decarboxylase B2RDU5 ornithine carbamoyltransferase A8K9P2 arginase P05089 Ornithine HMDB00214 Agmatine HMDB01432 Putrescine HMDB01414 ornithine decarboxylase 1 P11926 agmatine ureohydrolase (agmatinase) Q9BSE5 spermidine/spermine N1-acetyltransferase family member 2 Q96F10 S-Adenosylmethionine HMDB01185 amiloride binding protein 1 P19801 S-Adenosylmethioninamine HMDB00988 adenosylmethionine decarboxylase 1 Q5VXN4 N-Acetylputrescine HMDB02064 4-Aminobutyraldehyde HMDB01080 spermidine synthase B1AKP9 monoamine oxidase A P21397 aldehyde dehydrogenase 9 family, member A1 P49189 aldehyde dehydrogenase 2 family (mitochondrial)  P05091 5'-Methylthioadenosine HMDB01173 Gamma-Aminobutyric acid HMDB00112 N4-Acetylaminobutanal HMDB04226 glycine amidinotransferase P50440 aldehyde dehydrogenase 2 family (mitochondrial) P05091 Spermidine HMDB01257 spermine synthase P52788 4-Guanidinobutanoic acid HMDB03464 4-Acetamidobutanoic acid HMDB03681 Spermine HMDB01256 Glutamate Metabolism Beta-Alanine Metabolism